بیماری کاوازاکی: گزارش یک مورد با هیدروپس کیسه صفرا و کلستاز

ABSTRACT Kawasaki disease is an acute, febrile, systemic disease of unknown etiology which principally affects young children. Gallbladder hydrops is of rare complications of this disease. It appears that hydrops occurs more common in older children. The diagnosis is suggested by abdominal symptoms and abnormal results of liver function tests and confirmed by ultrasonography. Treatment is supportive and operative intervention is rarely recommended. The present case is a 30-month-old girl with gallbladder hydrops and cholestasis in addition to the characteristic signs and symptoms of kawasaki disease. Clinical features of the disease and treatment regimens, Including early administration of intravenous immune globulin (IVIG) which prevents cardiac complications are disdussed.